questions 2

Transposition of Great Vessels

Author:
Topic updated on 09/07/17 1:20am

Overview

Snapshot
  • A 24-hour-old newborn appears blue in all extremities, is cyanotic, and is transferred immediately to the NICU, where he is found to have a single, loud S2 murmur.
Introduction
  • Anatomic anomaly where the aorta arises from the right ventricle and the pulmonary artery arises from the left ventricle
    • leads to pulmonary and systemic circulation existing in parallel  
  • Infant must have arteriovenous communication to be compatible with life including
    • patent ductus arteriosus (PDA)
    • patent foramen ovale (PFO)
    • ventricular septal defect (VSD)
  • Risk factors are
    • diabetic mother
    • down's syndrome
    • Apert syndrome
    • cri-du-chat
    • trisomy 13/18
Presentation
  • Symptoms 
    • newborns are extremely cyanotic (blue skin) and are critically ill.
  • Physical exam
    • cyanosis
    • tachypnea
    • progressive respiratory failure
Evaluation
  • CXR shows enlarged egg-shaped heart, often referred to as "egg on a string"
Treatment
  • Prostaglandin E1 (PGE1) 
    • keeps PDA open until surgical repair is possible
  • Balloon atrial septostomy (Rashkind procedure)
    • must be performed if immediate surgery is not feasible
      • artificially creates ASD
      • allows oxygenated blood to travel between the ventricles to get to the aorta
  • Surgical correction 
    • is indicated in order for survival
    • can perform either arterial or atrial switch


  RATE CONTENT
5.0
AVERAGE 5.0 of 3 RATINGS

Qbank (0 Questions)

Sorry, this question is only available for Study Plan members.
Access to 600+ Questions not available in Free Qbank

This is a Never-Been-Seen Question that can only be seen in Study Plan Mock Exams.
Access to 600+ Questions not available in Free Qbank



Evidence & References Show References




Topic Comments

Subscribe status: